ATP6V1B1

Renal System · Distal Nephron Acid-Base Regulation

Why do cells spend energy moving hydrogen ions?

ATP6V1B1 makes a subunit of the energy-driven V-ATPase proton pump. Controlling proton movement allows cells to maintain the acidity needed for specialized functions.

Common Gene Name
ATPase H+ transporting V1 subunit B1
NCBI Gene ID
525
Chromosome
2

Clinical Evidence Status

Established disease relationship

These labels describe available evidence about a gene. They do not classify your variant or recommend a treatment.

Answer Sources

Explore supporting evidence (2 records)
Condition or drugEvidenceGrade / statusContextSource
renal tubular acidosis, distal, 2, with progressive sensorineural hearing lossClinGen gene-disease validityDefinitiveAutosomal recessiveView source
2026-02-18
Renal tubular acidosis with deafnessMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2014-03

Source snapshot: 2026-09-09. Consumer text updated: 2026-09-10. Source dates describe the cited records, not a new clinical review.

← Back to Renal System