CBS

Metabolic System · Vitamin, Cofactor & One-Carbon Metabolism

Does a CBS variant automatically call for vitamin B6?

CBS makes a vitamin-B6-dependent enzyme that helps convert homocysteine into another sulfur-containing compound. A common variant does not establish enzyme deficiency or a need for a particular supplement regimen.

Common Gene Name
cystathionine beta-synthase
NCBI Gene ID
875
Chromosome
21

Clinical Evidence Status

Actionability report availableEstablished disease relationshipTumor or drug-label biomarker context

These labels describe available evidence about a gene. They do not classify your variant or recommend a treatment.

Answer Sources

Explore supporting evidence (5 records)
Condition or drugEvidenceGrade / statusContextSource
classic homocystinuriaClinGen gene-disease validityDefinitiveAutosomal recessiveView source
2019-04-12
HomocystinuriaMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2011-07
Cystathionine Beta-Synthase DeficiencyClinGen clinical actionabilityScored report; not a validity gradeAdultView source
2023-10-06
Cystathionine Beta-Synthase DeficiencyClinGen clinical actionabilityScored report; not a validity gradePediatricView source
2023-10-06
BetaineFDA labeling biomarkerLabel mentions biomarker; actionability not inferredInborn Errors of MetabolismView source

Source snapshot: 2026-09-09. Consumer text updated: 2026-09-10. Source dates describe the cited records, not a new clinical review.

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