COL2A1

Musculoskeletal System · Chondrogenesis & Articular Cartilage Stability

Why can a cartilage gene also be relevant to eyes and hearing?

COL2A1 produces the building block of type II collagen. This collagen supports not only cartilage but also structures involved in normal eye and inner-ear development.

Common Gene Name
collagen type II alpha 1 chain
NCBI Gene ID
1280
Chromosome
12

Clinical Evidence Status

Established disease relationship

These labels describe available evidence about a gene. They do not classify your variant or recommend a treatment.

Answer Sources

Explore supporting evidence (12 records)
Condition or drugEvidenceGrade / statusContextSource
COL2A1-related spondyloepiphyseal dysplasiaClinGen gene-disease validityDefinitiveAutosomal dominantView source
2021-12-06
achondrogenesis type IIClinGen gene-disease validityDefinitiveAutosomal dominantView source
2020-10-05
Kniest dysplasiaClinGen gene-disease validityDefinitiveAutosomal dominantView source
2021-12-15
Stickler syndrome type 1ClinGen gene-disease validityDefinitiveAutosomal dominantView source
2023-09-28
dysplasia of the proximal femoral epiphysesClinGen gene-disease validityDefinitiveAutosomal dominantView source
2024-08-06
platyspondylic dysplasia, Torrance typeClinGen gene-disease validityDefinitiveAutosomal dominantView source
2021-02-01
spondyloperipheral dysplasiaClinGen gene-disease validityDefinitiveAutosomal dominantView source
2023-09-28
Stickler syndromeMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2024-12
Spondyloepiphyseal dysplasia congenitaMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2024-12
Spondyloepiphyseal dysplasia with marked metaphyseal changesMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2024-12
AchondrogenesisMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2024-12
Spondyloepiphyseal dysplasia with metatarsal shorteningMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2024-12

Source snapshot: 2026-09-09. Consumer text updated: 2026-09-10. Source dates describe the cited records, not a new clinical review.

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