COL4A1

Musculoskeletal System · Collagen Fibrillogenesis & Connective Tissue Tensile Strength

How is type IV collagen different from the collagen in tendons?

COL4A1 makes a component of type IV collagen, which forms flexible supporting networks. These networks are important in thin basement membranes beneath and around cells rather than simply forming thick tendon fibers.

Common Gene Name
collagen type IV alpha 1 chain
NCBI Gene ID
1282
Chromosome
13

Clinical Evidence Status

Established disease relationship

These labels describe available evidence about a gene. They do not classify your variant or recommend a treatment.

Answer Sources

Explore supporting evidence (5 records)
Condition or drugEvidenceGrade / statusContextSource
COL4A1-related disorderClinGen gene-disease validityDefinitiveAutosomal dominantView source
2024-02-12
Anophthalmia/MicrophthalmiaMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2011-09
COL4A1-related brain small-vessel diseaseMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2011-09
Familial porencephalyMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2011-09
Hereditary angiopathy with nephropathy, aneurysms, and muscle cramps syndromeMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2011-09

Source snapshot: 2026-09-09. Consumer text updated: 2026-09-10. Source dates describe the cited records, not a new clinical review.

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