KCNJ11

Nervous System · Neuronal Excitability & Ion Flux

How does a potassium channel help control insulin release?

KCNJ11 makes a channel component that partners with the ABCC8 product in pancreatic beta cells. The channel links the cell's energy state with signals controlling insulin secretion.

Common Gene Name
potassium inwardly rectifying channel subfamily J member 11
NCBI Gene ID
3767
Chromosome
11

Clinical Evidence Status

Established disease relationship

These labels describe available evidence about a gene. They do not classify your variant or recommend a treatment.

Answer Sources

Explore supporting evidence (7 records)
Condition or drugEvidenceGrade / statusContextSource
monogenic diabetesClinGen gene-disease validityDefinitiveAutosomal dominantView source
2023-01-05
hyperinsulinemic hypoglycemia, familial, 2ClinGen gene-disease validityDefinitiveAutosomal recessiveView source
2026-03-03
hyperinsulinemic hypoglycemia, familial, 2ClinGen gene-disease validityLimitedAutosomal dominantView source
2026-06-02
Congenital hyperinsulinismMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2026-01
Permanent neonatal diabetes mellitusMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2026-01
Gestational diabetesMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2026-01
Maturity-onset diabetes of the youngMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2026-01

Source snapshot: 2026-09-09. Consumer text updated: 2026-09-10. Source dates describe the cited records, not a new clinical review.

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