NDUFV1

Metabolic System · Mitochondrial Electron Transport & Oxidative Phosphorylation

How does NDUFV1 help mitochondria start extracting usable energy?

NDUFV1 makes part of respiratory complex I that participates in handling electrons from NADH. Those electrons enter a chain of reactions that supports cellular energy production.

Common Gene Name
NADH:ubiquinone oxidoreductase core subunit V1
NCBI Gene ID
4723
Chromosome
11

Clinical Evidence Status

Established disease relationship

These labels describe available evidence about a gene. They do not classify your variant or recommend a treatment.

Answer Sources

Explore supporting evidence (2 records)
Condition or drugEvidenceGrade / statusContextSource
Leigh syndromeClinGen gene-disease validityDefinitiveAutosomal recessiveView source
2019-11-26
mitochondrial diseaseClinGen gene-disease validityDefinitiveAutosomal recessiveView source
2024-05-20

Source snapshot: 2026-09-09. Consumer text updated: 2026-09-10. Source dates describe the cited records, not a new clinical review.

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