NR5A1

Reproductive System · Sex Determination & Gonadal Differentiation

Why can NR5A1 affect both reproductive and adrenal tissues?

NR5A1 encodes steroidogenic factor 1, a regulator of genes involved in gonadal and adrenal development. Its shared role links these tissues with the production of steroid hormones.

Common Gene Name
nuclear receptor subfamily 5 group A member 1
NCBI Gene ID
2516
Chromosome
9

Clinical Evidence Status

Established disease relationship

These labels describe available evidence about a gene. They do not classify your variant or recommend a treatment.

Answer Sources

Explore supporting evidence (3 records)
Condition or drugEvidenceGrade / statusContextSource
NR5A1-related sex development disorderClinGen gene-disease validityDefinitiveAutosomal dominantView source
2026-01-21
46,XX testicular disorder of sex developmentMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2015-03
Swyer syndromeMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2015-03

Source snapshot: 2026-09-09. Consumer text updated: 2026-09-10. Source dates describe the cited records, not a new clinical review.

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