PMS2

Universal Cellular Machinery · DNA Damage Repair & Genomic Integrity

What is PMS2's job after a DNA-copying error is found?

PMS2 makes a mismatch-repair protein that works with MLH1. Their complex coordinates correction of the error, helping protect the accuracy of DNA passed to new cells.

Common Gene Name
PMS1 homolog 2, mismatch repair system component
NCBI Gene ID
5395
Chromosome
7

Clinical Evidence Status

Actionability report availableEstablished disease relationship

These labels describe available evidence about a gene. They do not classify your variant or recommend a treatment.

Answer Sources

Explore supporting evidence (7 records)
Condition or drugEvidenceGrade / statusContextSource
Lynch syndromeClinGen gene-disease validityDefinitiveAutosomal dominantView source
2022-12-30
hereditary breast carcinomaClinGen gene-disease validityDisputedAutosomal dominantView source
2023-12-21
mismatch repair cancer syndrome 1ClinGen gene-disease validityDefinitiveAutosomal recessiveView source
2022-12-30
Constitutional mismatch repair deficiency syndromeMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2025-05
Mismatch repair cancer syndrome (MMRCS)ClinGen clinical actionabilityScored report; not a validity gradeAdultView source
2022-12-06
Lynch SyndromeClinGen clinical actionabilityScored report; not a validity gradeAdultView source
2023-06-28
Mismatch repair cancer syndrome (MMRCS)ClinGen clinical actionabilityScored report; not a validity gradePediatricView source
2024-03-24

Source snapshot: 2026-09-09. Consumer text updated: 2026-09-10. Source dates describe the cited records, not a new clinical review.

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