PTCH1

Developmental System · Morphogenesis & Embryonic Axis Patterning

How does PTCH1 help keep cell growth under control?

PTCH1 makes a receptor in the Hedgehog signaling pathway, which helps organize developing tissues. Certain pathogenic variants disrupt this regulation and are associated with nevoid basal cell carcinoma syndrome.

Common Gene Name
patched 1
NCBI Gene ID
5727
Chromosome
9

Clinical Evidence Status

Actionability report availableEstablished disease relationship

These labels describe available evidence about a gene. They do not classify your variant or recommend a treatment.

Answer Sources

Explore supporting evidence (8 records)
Condition or drugEvidenceGrade / statusContextSource
nevoid basal cell carcinoma syndromeClinGen gene-disease validityDefinitiveAutosomal dominantView source
2018-06-04
holoprosencephalyClinGen gene-disease validityLimitedAutosomal dominantView source
2025-07-09
Gorlin syndromeMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2012-10
Nonsyndromic holoprosencephalyMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2012-10
ColobomaMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2012-10
9q22.3 microdeletionMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2012-10
Basal Cell Nevus Syndrome (BCNS)ClinGen clinical actionabilityScored report; not a validity gradeAdultView source
2023-03-07
Basal Cell Nevus Syndrome (BCNS)ClinGen clinical actionabilityScored report; not a validity gradePediatricView source
2023-03-07

Source snapshot: 2026-09-09. Consumer text updated: 2026-09-10. Source dates describe the cited records, not a new clinical review.

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