RUNX1

Hematologic System · Hematopoiesis, Erythropoiesis & Iron Homeostasis

Why would RUNX1 be investigated in a family with blood-cell problems?

RUNX1 makes a DNA-binding regulator that controls genes involved in blood-cell development. A confirmed pathogenic finding can be relevant to inherited blood disorders, with interpretation depending on the family's clinical pattern.

Common Gene Name
RUNX family transcription factor 1
NCBI Gene ID
861
Chromosome
21

Clinical Evidence Status

Actionability report availableEstablished disease relationship

These labels describe available evidence about a gene. They do not classify your variant or recommend a treatment.

Answer Sources

Explore supporting evidence (7 records)
Condition or drugEvidenceGrade / statusContextSource
hereditary thrombocytopenia and hematologic cancer predisposition syndromeClinGen gene-disease validityDefinitiveAutosomal dominantView source
2018-06-04
Juvenile idiopathic arthritisMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2013-11
Core binding factor acute myeloid leukemiaMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2013-11
Cytogenetically normal acute myeloid leukemiaMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2013-11
Systemic mastocytosisMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2013-11
Hereditary thrombocytopenia and hematological cancer predisposition syndromeClinGen clinical actionabilityScored report; not a validity gradeAdultView source
2022-02-09
Hereditary thrombocytopenia and hematological cancer predisposition syndromeClinGen clinical actionabilityScored report; not a validity gradePediatricView source
2022-02-09

Source snapshot: 2026-09-09. Consumer text updated: 2026-09-10. Source dates describe the cited records, not a new clinical review.

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