RYR1

Musculoskeletal System · Excitation-Contraction Coupling

How does a skeletal muscle release calcium to start contracting?

RYR1 makes a channel that releases calcium from stores inside muscle cells. The released calcium helps trigger the machinery that produces muscle contraction.

Common Gene Name
ryanodine receptor 1
NCBI Gene ID
6261
Chromosome
19

Clinical Evidence Status

Actionability report availableEstablished disease relationshipTumor or drug-label biomarker context

These labels describe available evidence about a gene. They do not classify your variant or recommend a treatment.

Answer Sources

Explore supporting evidence (14 records)
Condition or drugEvidenceGrade / statusContextSource
malignant hyperthermia, susceptibility to, 1ClinGen gene-disease validityDefinitiveAutosomal dominantView source
2020-11-25
RYR1-related myopathyClinGen gene-disease validityDefinitiveAutosomal recessiveView source
2020-07-27
RYR1-related myopathyClinGen gene-disease validityDefinitiveAutosomal dominantView source
2020-10-26
Central core diseaseMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2020-03
Malignant hyperthermiaMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2020-03
Multiminicore diseaseMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2020-03
Congenital fiber-type disproportionMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2020-03
Centronuclear myopathyMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2020-03
Malignant Hyperthermia SusceptibilityClinGen clinical actionabilityScored report; not a validity gradeAdultView source
2022-02-09
Malignant Hyperthermia SusceptibilityClinGen clinical actionabilityScored report; not a validity gradePediatricView source
2022-02-09
DesfluraneFDA labeling biomarkerLabel mentions biomarker; actionability not inferredAnesthesiologyView source
IsofluraneFDA labeling biomarkerLabel mentions biomarker; actionability not inferredAnesthesiologyView source
SevofluraneFDA labeling biomarkerLabel mentions biomarker; actionability not inferredAnesthesiologyView source
Succinylcholine (2)FDA labeling biomarkerLabel mentions biomarker; actionability not inferredAnesthesiologyView source

Source snapshot: 2026-09-09. Consumer text updated: 2026-09-10. Source dates describe the cited records, not a new clinical review.

← Back to Musculoskeletal System