USH2A

Sensory System · Phototransduction & Retinal Processing

Why can USH2A be relevant to both hearing and vision?

USH2A makes usherin, a protein present in supporting structures in the inner ear and retina. Its use in both tissues helps explain why certain pathogenic variants can affect more than one sense.

Common Gene Name
usherin
NCBI Gene ID
7399
Chromosome
1

Clinical Evidence Status

Established disease relationship

These labels describe available evidence about a gene. They do not classify your variant or recommend a treatment.

Answer Sources

Explore supporting evidence (3 records)
Condition or drugEvidenceGrade / statusContextSource
Usher syndrome type 2ClinGen gene-disease validityDefinitiveAutosomal recessiveView source
2017-02-15
Usher syndromeMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2016-05
Retinitis pigmentosaMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2016-05

Source snapshot: 2026-09-09. Consumer text updated: 2026-09-10. Source dates describe the cited records, not a new clinical review.

← Back to Sensory System