WT1

Renal System · Glomerular Filtration Barrier

Why can WT1 connect kidney development with later kidney function?

WT1 controls genes needed to form the kidneys and gonads before birth. It also remains important in the kidney's filtering structures after birth.

Common Gene Name
WT1 transcription factor
NCBI Gene ID
7490
Chromosome
11

Clinical Evidence Status

Actionability report availableEstablished disease relationship

These labels describe available evidence about a gene. They do not classify your variant or recommend a treatment.

Answer Sources

Explore supporting evidence (10 records)
Condition or drugEvidenceGrade / statusContextSource
Wilms tumor 1ClinGen gene-disease validityDefinitiveAutosomal dominantView source
2020-07-30
Denys-Drash syndromeClinGen gene-disease validityDefinitiveAutosomal dominantView source
2021-07-27
46,XX testicular disorder of sex developmentMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2018-09
WAGR syndromeMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2018-09
Frasier syndromeMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2018-09
Cytogenetically normal acute myeloid leukemiaMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2018-09
Prostate cancerMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2018-09
Congenital nephrotic syndromeMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2018-09
Wilms tumorMedlinePlus related conditionAssociation type varies; no grade assigned hereView source
2018-09
Wilms tumorClinGen clinical actionabilityScored report; not a validity gradePediatricView source
2022-02-09

Source snapshot: 2026-09-09. Consumer text updated: 2026-09-10. Source dates describe the cited records, not a new clinical review.

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